Figure 1. A six-year old white male presented for low vision rehabilitation with a history of X-linked retinoschisis (XLRS). He reported blurred vision for a year. His medical history was unremarkable. His family ocular history was positive for X-lined retinoschisis, including a brother and an uncle

Figure 2. A&B. Fundus images showing stellar maculopathy OD/OS.

Figure 3. OCT illustrating macular thickening of both maculae. A split of the inner retinal layer from the outer retinal layers is also illustrated.

Figure 4. ERG exemplifying a mildly electronegative response. (Image courtesy Jerome Sherman, OD, FAAO)

Figure 5. OCT of OS (lower) showing both reduced macular thickness restoration of the retinal contour. Compare with Figure 2.